Findings
Fat density lesion within the pericavernous region in the region of Meckel’s cave extending inferiorly into the posterior fossa. Scattered lipid droplets throughout the subarachnoid space.
Differential diagnosis:
- Dermoid cyst
- Epidermoid cyst
- Craniopharyngioma
- Teratoma
- Lipoma
Diagnosis: Ruptured intracranial dermoid
Key points
Congenital inclusion cyst.
Epidemiology: Rare; <0.5% of primary intracranial tumors.
30-50 y/o.
Presentation (uncomplicated): HA (32%), Seizure (30%), rarely with DI, hypopituitarism, visual defects.
Benign, slow growing.
Rare malignant transformation into SCCa.
Increased risk of rupture with increased size.
Significant M&M with rupture: chemical meningitis, seizures, coma, vasospasm, etc.
Fat density distinguishes from epidermoid (usually CSF density).
Scattered lipid droplets in subarachnoid/ventricles with rupture.
20 % have capsular calcium.
Most supratentorial, midline or near midline.
Other sites: spine, orbit.
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